DOI: http://dx.doi.org/10.18203/issn.2455-4510.IntJResOrthop20204603

Large intramuscular plexiform neurofibroma of thigh: a multidisciplinary team approach

Aminda Mandal, Satyam Kumar, Avinash K. Sinha, Deepak Kumar, Prabhat K. Dwivedi, Nikesh D. Panchbhai, Lavleen Pandey

Abstract


Large plexiform neurofibroma of lower extremity involving the muscle is a rare entity. In this article we present the case of plexiform neurofibroma of right thigh involving the muscular plane and entrapment of the sciatic nerve. A 28 year lady presented with a plexiform neurofibroma of right thigh of size 60 cm×30 cm×25 cm with a positive family history of neurofibromatosis type 1. MRI was done for the assessment of the tumour and the adjacent structure involvement. The neurofibroma was removed with a multidisciplinary team approach with an intensive peri operative management. The pathological diagnosis was plexiform neurofibroma with diffuse neurofibroma. We have reported a rare case of large plexiform neurofibroma of lower extremity with muscle involvement and nerve entrapment.


Keywords


Neurofibromatosis, Plexiform neurofibroma, Schwannoma, Intramuscular, Von Recklinghausen

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